Alpha thalassemia is the result of deficient or absent syn thesis of alpha globin chains, leading to excess beta glo bin chains. Abstract hereditary thalassemic syndromes are characterized by variable deficiencies in the production of normal hemoglobin chains. Talasemia alfa talasemias h en una familia mestiza mexicana. Alphathalassaemia is inherited as an autosomal recessive disorder characterised by a microcytic hypochromic anaemia, and a clinical phenotype varying from almost asymptomatic to a lethal haemolytic anaemia. Diferencias entre alfa y beta talasemia mi remedio casero. Undefined cases in this group of cases, several possibilities can be considered. Carriers are often referred to as having thalassemia minor or. Defi cient production is usually caused by a deletion of one or more of these genes. Alpha globin chain production is controlled by two genes on each chromosome 16 table 14,5. Estos pacientes suelen presentar una anemia moderada.
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